Nursing care process in patients with Noonan syndrome and its stages

Abstract

The syndrome of Noonan was described in 1963 by Noonan and Ehmke in patient with estenosis lung valvular, associated to low stature, hipertelorism and moderate mental retard, among other alterations. The author evidence the way of nursing performance before a patient with Syndrome of Noonam in the first level of attention. Was carried out a presentation of a clinical case with Syndrome Noonam diagnosed by the personnel specialized in Clinical Genetics. Evidencing the way of infirmary performance by means of the identification and establishment of priorities of the necessities of the pyramid of Kalish and Maslow in the nursing care plan with the implementation of the diagnoses nurses accepted for the development and clinical validation 2015-2017. It was possible to present through the nursing care plan, acting of nursing through the body of nursing knowledge and their cares that guarantee a group of actions of prevention to diminish the risks characteristic of the patient with syndrome of Noonam. Finaly evidence that with the way of nursing performance and the actions of the plan of cares diminish the risks and he/she improves the interaction with other specialties that they help to the patient's rehabilitation with Syndrome of Noonam in the first level of attention.